Vertebral artery tortuosity in Turner syndrome: is tortuosity a component of the aortopathy phenotype?
نویسندگان
چکیده
Background Turner syndrome is associated with bicuspid aortic valve (BAV), coarctation of the aorta, aortic dilation, and aortic dissection. Vertebral artery tortuosity, as demonstrated by magnetic resonance angiography (MRA), is increased in other disorders associated with thoracic aortic dilation and dissection, including Marfan syndrome and Loeys-Dietz syndrome, and increased tortuosity is associated with earlier adverse cardiovascular outcomes in those groups. We investigated the association between vertebral artery tortuosity and aortic pathology in patients with Turner syndrome.
منابع مشابه
Arterial tortuosity and change with age in young patients with aortopathy
Background In pilot studies, increased vascular tortuosity is associated with adverse outcomes in children and young adults withheritable thoracic aortic disease, specifically Marfan syndrome (MFS) and Loeys Dietz syndrome (LDS). It is known that vertebral artery tortuosity is highly prevalent in older adults who do not have heritable thoracic aortic disease. We hypothesized that tortuosity inc...
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